Main Article Content

Churg-Strauss syndrome associated with AA amyloidosis: a case report


Mouna Maamar
Zoubida Tazi-Mezalek
Hicham Harmouche
Zitouna El Hamany
Mohammed Adnaoui
Mohammed Aouni

Abstract

Churg Strauss syndrome is a rare systemic and pulmonary vasculitis exceptionally associated with AA amyloidosis. We report the case of a 65-year old woman with past medical history of asthma. She developed polyarthralgia, headache and purpura. A laboratory workout found hypereosinophilia (1150/μL), positive p-ANCA, microscopic haematuria and proteinuria at 2g/day. A diagnosis of Churg-Strauss syndrome was established based on five criteria of the American College of Rheumatology (ACR). Renal biopsy showed an important type AA amyloid deposit. The patient was treated with steroids with a good response of the vasculitis and amyloidosis with disappearance of the proteinuria.

Pan African Medical Journal 2012; 12:30

Journal Identifiers


eISSN: 1937-8688