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Dental, dermatological and radiographic findings in a case of Gorlin-Goltz Syndrome: report and review


Kumar Nilesh
Shivsagar Tewary
Sameer Zope
Jinesh Patel
Aaditee Vande

Abstract

Gorlin-Goltz syndrome (GGS) is a rare autosomal dominant disorder. The disease shows multiple organ involvement with variable clinical presentation. Thus a multidisciplinary approach is required for its prompt clinical diagnosis and management of this condition. This paper highlights a case of GGS presenting in a young male patient with cranial, facial, dermatological, dental and skeletal involvement. The diagnosis of the syndrome was based on its clinical presentation, radiological features and histopathological findings. A review of the diagnostic criteria is also presented.

Keywords: Nevoid basal cell carcinoma syndrome, kertocystic odontogenic tumor


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eISSN: 1937-8688