Long survival ( 21 years) after portoenterostomy for biliary atresia: A case report and review of complications

Abstract

Long term survival for decades after portoenterostomy (Kasai procedure) for biliary atresia is rare and the association of portoenterostomy with liver cirrhosis is well known. Not much attention was given in the evaluation of the imaging features of cirrhosis caused by portoenterostomy as received by other known usual causes of cirrhosis. We presented a case of a Nigerian with confirmed biliary atresia at birth, that suvived portoenterostomy performed at two months of age for 21years. The cirrhotic presentation at imaging was that of prominent volume redistribution with less parenchymal changes in the liver. The long term survival and the type of cirrhotic presentation on imaging in this case is worthy of note for the record.