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A rare case of intestinal obstruction secondary to metastasis dermatofibrosarcoma protuberans
Abstract
Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue sarcoma, which arises from the dermis. It behaves as a low to intermediate-grade malignancy, is locally aggressive, and frequently has local recurrence but rarely metastasize. The most common organ of metastasis reported is the lungs. Here we present a rare case of metastasis dermatofibrosarcoma protuberans (DFSP) that presents with intra-abdominal mass causing intestinal obstruction. Exploratory laparotomy and en-bloc resection of the tumor were done followed by adjuvant chemotherapy.