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A rare case of intestinal obstruction secondary to metastasis dermatofibrosarcoma protuberans


Syibrah Khuzaimah Zahid
Wan Muhamad Mokhzani
Ahmad Fardi Sulaiman
Wan Zainira Wan Zain
Siti Zarqah Omar

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue sarcoma, which arises from the dermis. It behaves as a low to intermediate-grade malignancy, is locally aggressive, and frequently has local recurrence but rarely metastasize. The most common organ of metastasis reported is the lungs. Here we present a rare case of metastasis dermatofibrosarcoma protuberans (DFSP) that presents with intra-abdominal mass causing intestinal obstruction. Exploratory laparotomy and en-bloc resection of the tumor were done followed by adjuvant chemotherapy.


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eISSN: 2415-2420
print ISSN: 0014-1755