Prune belly syndrome: A rare congenital malformation in a 6-year-old Ugandan boy

Abstract

A 6 year male presented with history of recurrent urinary tract infections since birth. At the time of presentation he had an active urinary tract infection associated with deranged renal function tests, a soft wrinkled abdomen and bilateral undescended testis. Further evaluation with an abdominal ultrasound scan confirmed a diagnosis of prune belly syndrome. He was managed for the urine infection, had a urethral catheter for ureter decompression inserted and put on maintenance antibiotics. There are few re­ports about this condition in Uganda and hence this case can advance knowledge on this rare syndrome.