Bilateral multicystic dysplastic kidneys: Case report

Abstract

Multicystic dysplastic kidney (MCDK) is a congenital, non-heritable maldevelopment in which the renal cortex is replaced by numerous cysts of varying sizes. Typically, MCDK is a unilateral disorder in 76% of cases and bilateral in 24%. The latter is incompatible with life. We present the case of a male child with bilateral MCDK who was followed up with ultrasound scan (USS) from 22nd week of intrauterine life till death on the 19th day after delivery. Serial antenatal USS revealed oligohydramnios and both kidneys showed multiple cysts which appeared to be communicating. Postnatal USS however, revealed multiple sub-cortical thin walled cysts of varying sizes which apparently appeared to be communicating. A diagnosis of bilateral MCDK was made and was confirmed at autopsy.