Sickle cell anemia with acute splenic sequestration

Abstract

A three and half years old girl, a known sickler presented with abdominal pain of four days, vomiting, cough and fever of three days. She had history of chest infections and fever which were treated as pneumonia. On examination she was febrile, had a tinge of jaundice, severe palmor pallor, hepatomegally with span of 11 cm, enlarged spleen 5 cm below costal margin. Respiratory rate was 40/min and crackles were heard on the lower right lung. Pulse rate was 130 beats/min, regular and gallop rhythm was present. Diagnosis of acute splenic sequestration syndrome and non-severe pneumonia was made. Packed cell volume blood transfusion was done twice and antibiotics were given. She was discharged after five days stay in the hospital.