Giant Dermatofibrosarcoma: A case report

Abstract

Dermatofibrosarcoma Protuberans (DFSP) is a rare skin tumour with high recurrences. World Health Organization report has shown it to  be a slow growing, nodular neoplasm of intermediate grade malignancy that is found almost exclusively in the dermis from where it often invades the subcutaneous tissue. It is more common in adults than children, in blacks than whites and on the trunk than other  parts of the body. Management is challenging due to its propensity to recur after local wide excision and for this reason, it is believed that  combining either wide local excision with Mohs micrographic surgery or adjuvant chemotherapy or radiation therapy may reduce its  recurrence. In this follow up case report, we present a 53 year old man who had wide local excision of his recurrent facial DFSP  14months post-surgery. His past medical history has shown that the man has had this tumour excised 13 times in other hospitals prior to  his first presentation to us 14 months ago. In multiple recurrences with previous surgical scars in which free margin is doubtful as noticed  in our case, adjuvant radiotherapy will be of benefit. This was recommended to the patient during his first surgery but could not  have it done due to some logistics reasons.