Megacystis microcolon intestinal hypoperistalsis syndrome: a report of a variant

Abstract

Megacystis microcolon intestinal hypoperistalsis syndrome is a very rare cause of functional intestinal obstruction in newborns. It is associated with nonobstructed distended urinary bladder, microcolon, and decreased or absent intestinal peristalsis. The prognosis is poor and most patients die early because of sepsis or total parental nutrition-related complications. This report describes a new case of megacystis microcolon intestinal hypoperistalsis syndrome associated with meconium ileus, dilated stomach, and megaesophagus.

Keywords: intestinal hypoperistalsis syndrome, megacystis, microcolon