Ruptured hepatoblastoma treated with primary surgical resection

Abstract

The aim of this study was to review two cases of ruptured hepatoblastoma treated with primary surgical resection. Hepatoblastoma is the most common primary liver malignancy of childhood, although it remains infrequent. A rare, but serious condition is when the tumor presents with spontaneous rupture. This is a well-known phenomenon; however, it is rarely reported in the literature, and the long-term outcomes of various management strategies are currently unclear. We present two cases of patients in whom primary surgical resection was performed and discuss outcomes, and also present a current literature review. Children with ruptured hepatoblastoma treated with emergency primary surgical resection, followed by adjuvant chemotherapy, may have favorable outcomes.

Keywords: hepatoblastoma, rupture, surgical resection